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A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation

Identifieur interne : 000841 ( Main/Exploration ); précédent : 000840; suivant : 000842

A primary intestinal lymphangiectasia hiding the diagnosis of pleural and pericardial tuberculosis: a clinical observation

Auteurs : Sanaa Hammi [Maroc] ; Hajar Berrani [Maroc] ; Thami Benouchen [Maroc] ; Naima Lamlami [Maroc] ; Imane Elkhiyat [Maroc] ; Jamal Eddine Bourkadi [Maroc]

Source :

RBID : PMC:5409999

Descripteurs français

English descriptors

Abstract

Primary intestinal lymphangiectasia (Waldmann’s disease) is an exudative enteropathy characterized by lymph leakage into the small bowel lumen leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia (particularly T-cell). The diagnosis is based on viewing the duodenal lymphangiectasia. A 20 years old female patient, treated for a primary intestinal lymphangiectasia, has consulted for anasarca. Etiological work-up reveals pleural and pericardial tuberculosis. The clinical aggravation of an enteropathy, particularly in adulthood, requires a search for a secondary etiology. Tuberculosis should be sought systematically.


Url:
DOI: 10.11604/pamj.2017.26.89.11125
PubMed: 28491220
PubMed Central: 5409999


Affiliations:


Links toward previous steps (curation, corpus...)


Le document en format XML

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<p>Primary intestinal lymphangiectasia (Waldmann’s disease) is an exudative enteropathy characterized by lymph leakage into the small bowel lumen leading to hypoalbuminemia, hypogammaglobulinemia and lymphopenia (particularly T-cell). The diagnosis is based on viewing the duodenal lymphangiectasia. A 20 years old female patient, treated for a primary intestinal lymphangiectasia, has consulted for anasarca. Etiological work-up reveals pleural and pericardial tuberculosis. The clinical aggravation of an enteropathy, particularly in adulthood, requires a search for a secondary etiology. Tuberculosis should be sought systematically.</p>
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